LETTERS TO THE EDITOR CARTAS AO EDITOR

Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report

Oclusão unilateral da artéria central da retina como único sinal de apresentação da síndrome de Susac em jovem do sexo masculino: relato de caso

Robert Alex Egan

Physician, Oregon Neurology, Tualatin, Unite States

Correspondence address

I read with interest the report of "Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report" by Apóstolos-Pereira et al.⁽¹⁾ Central retinal artery occlusion is very rare in Susac syndrome as evidenced by the paucity of reports in the clinical literature. The corpus callosum findings in this case are pathognomonic for the disease with the central callosal lesion and the 2 small spoke lesions in the posterior callosum. However, the fundus appearance is somewhat odd with the significant platelet-like embolic material in the arterioles. These are not Gass plaques as has been described previously⁽²⁾. Did they disappear after his initial presentation? There are also characteristic fluorescein angiographic findings described previously⁽³⁾. Was the typical autofluorescense pattern located remotely from the retinal artery occlusion? I am particularly interested in learning if the right eye showed this pattern prior to infarction; if so, can this be published? Were anti-endothelial cell antibodies sent?

REFERENCES

1. Apostolos-Pereira SL dos, Kara-Jose LB, Marchiori PE, Monteiro ML. Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report. Arq Bras Oftalmol. 2013;76(3):192-4.         

2. Egan RA, Ha Nguyen T, Gass JD, Rizzo JF 3^rd, Tivnan J, Susac JO. Retinal artery wall plaques in Susac Syndrome. Am J Ophthalmol. 2003;135(4):483-6.         

3. Egan RA, Hills WL, Susac JO. Gass plaques and fluorescein leakage in Susac Syndrome. J Neurol Sci. 2010;299(1-2):97-100.         

Corresponding author:
Robert Alex Egan.
Director of Neuro-Ophthalmology.
Oregon Neurology - 19260 SW 65^th Ave, Ste 280 - Tualatin, OR, United States, 97062
E-mail: [email protected]

Submitted for publication: August 21, 2013
Accepted for publication: August 25, 2013
Funding: No specific financial support was available for this study.
Disclosure of potential conflicts of interest: R.A.Egan, None.